Cystic Fibrosis By Rnpedia.Com

Cystic fibrosis is treated by:         

• Airway clearance techniques that aim to move the thick mucus from the lungs

• Taking special vitamins

• Taking pancreatic enzymes to help digest food

• All of these

Is there a cure for Cystic Fibrosis?

• True

• False

 The nurse in charge is reviewing a patient’s prenatal history. Which finding indicates a genetic risk factor? 

• The patient is 25 years old

• The patient has a child with cystic fibrosis

• The patient was exposed to rubella at 36 weeks’ gestation

• The patient has a history of preterm labor at 32 weeks’ gestation

Cystic fibrosis is diagnosed by:         

• Echocardiogram

• Complete blood panel

• Chest X-ray

• Sweat test

A client with cystic fibrosis is taking pancreatic enzymes. The nurse should administer this medication:   

• Once per day in the morning

• Three times per day with meals

• Once per day at bedtime

• Four times per day

Which of the following clients is at high risk for developmental problem? 

• A toddler with acute Glomerulonephritis on antihypertensive and antibiotics

• A 5-year-old with asthma on cromolyn sodium

• A preschooler with tonsillitis

• A 2 1/2 –year old boy with cystic fibrosis

When administering pancrelipase (Pancreases capsules) to child with cystic fibrosis, nurse Faith knows they should be given: 

• With meals and snacks

• Every three hours while awake

• On awakening, following meals, and at bedtime

• After each bowel movement and after postural drainage

Cystic fibrosis is caused by:         

• A defective gene that causes abnormalities in the brain

• It is not known what the cause is

• Someone who eats too much salt

• A defective gene that leads to the making of an abnormal protein

At what age is this disease diagnosed?

• Early years [0-5]

• Childhood years [5-12]

• Teenage years [12-17]

• Adult years [18-50]

• 50+

The foul-smelling, frothy characteristic of the stool in cystic fibrosis results from the presence of large amounts of which of the following: 

• sodium and chloride

• Undigested fat

• Semi-digested carbohydrates

• lipase, trypsin and amylase

A 6-year-old with cystic fibrosis has an order for Creon. The nurse knows that the medication will be given:

• At bedtime

• With meals and snacks

• Twice daily

• Daily in the morning

One of the most important pulmonary treatments in cystic fibrosis is:

• Inhaled beta agonists.

• Inhaled corticosteroids.

• Chest physiotherapy.

• Oral enzymes.

 A child with cystic fibrosis is being treated with inhalation therapy with Pulmozyme (dornase alfa). A side effect of the medication is:

• Weight gain

• Hair loss

• Sore throat

• Brittle nails

The nurse is teaching the mother of a child with cystic fibrosis how to do postural drainage. The nurse should tell the mother to:

• Use the heel of her hand during percussion

• Change the child’s position every 20 minutes

• Do percussion after the child eats and at bedtime

• Use cupped hands during percussion

  The mother of a child with cystic fibrosis tells the nurse that her child makes "snoring" sounds when breathing. The nurse is aware that many children with cystic fibrosis have:

• Choanal atresia

• Nasal polyps

• Septal deviations

• Enlarged adenoids

A male adult client with cystic fibrosis is admitted to an acute care facility with an acute respiratory infection. Prescribed respiratory treatment includes chest physiotherapy. When should the nurse perform this procedure?  

• Immediately before a meal

• At least 2 hours after a meal

• When bronchospasms occur

• When secretions have mobilized

The nurse is providing a health teaching to the mother of an 8-year-old child with cystic fibrosis. Which of the following statement if made by the mother would indicate to the nurse the need for further teaching about the medication regimen of the child? 

• “My child might need an extra capsule if the meal is high in fat”

• “I’ll give the enzyme capsule before every snack”

• “I’ll give the enzyme capsule before every meal”

• “My child hates to take pills, so I’ll mix the capsule into a cup of hot chocolate

 The recommended diet for someone with cystic fibrosis is:        

• High calorie and high fat diet

• High fat diet

• Low fat diet

• High calorie diet

If one of your parents have the disease does that mean you have a chance of getting the infection?

• True

• False

An 8-year-old client with cystic fibrosis is admitted to the hospital and will undergo a chest physiotherapy treatment. The therapy should be properly coordinated by the nurse with the respiratory therapy department so that treatments occur during: 

• After meals

• Between meals

• After medication

• Around the child’s play schedule

A 2-year-old client with cystic fibrosis is confined to bed and is not allowed to go to the playroom. Which of the following is an appropriate toy would the nurse select for the child: 

• Puzzle

• Musical automobile

• Arranging stickers in the album

• Pounding board and hammer

A child who has recently been diagnosed with cystic fibrosis is in a pediatric clinic where a nurse is performing an assessment. Which later finding of this disease would the nurse not expect to see at this time?

• Positive sweat test

• Bulky greasy stools

• Moist, productive cough

• Meconium ileus

Which of the following is the approximate prevalence ratio for cystic fibrosis?  

• 1: 25,000

• 1: 5,000

• 1: 2,000

• 1: 800

Cystic fibrosis is also called:        

• Bronchiectasis

• Sticky mucus disease

• Mucovicidosis

• Irritating cough disease

Cystic Fibrosis is a