Metabolism Test: Trivia Questions! Quiz

36 Questions | Total Attempts: 402

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Metabolism Test: Trivia Questions! Quiz - Quiz

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Questions and Answers
  • 1. 
    Most metabolic diseases are inherited by which genetic transmission?
    • A. 

      Autosomal dominant

    • B. 

      Autosomal recessive

    • C. 

      X-linked

    • D. 

      All the above

  • 2. 
    Which of the following is NOT a mechanism for genetic transmission?
    • A. 

      Chromatinization

    • B. 

      Autosomal dominant

    • C. 

      Autosomal recessive

    • D. 

      X-linked

    • E. 

      A and D

  • 3. 
    Which of the following is NOT a DNA Nucleotide?
    • A. 

      Thymine

    • B. 

      Methionine

    • C. 

      Cytosine

    • D. 

      Adenosine

  • 4. 
    In autosomal recessive disorders what is the percentage that a child with be affected with a disorder (homozygous-gets both "bad" genes)?
    • A. 

      5%

    • B. 

      15%

    • C. 

      30%

    • D. 

      25%

  • 5. 
    In treating patients with inborn errors of metabolism which of the following is not a principle in management?
    • A. 

      Reduce the amount of "substrate" (diet and catabolism)

    • B. 

      Reduce the amount of "product" that is blocked in the pathway

    • C. 

      Reduce the amount of catabolism that can add to substrate

    • D. 

      Supplement with coenzymes, if needed

  • 6. 
    Without diet therapy, levels of blood and brain phenylalanine are decreased in PKU.
    • A. 

      True

    • B. 

      False

  • 7. 
    Patients calculate phenylalanine intake:
    • A. 

      In exchanges of 15 mg phenylalanine

    • B. 

      Every mg of phenylalanine

    • C. 

      In grams of protein

    • D. 

      All of the above is possible

  • 8. 
    It is recommended a PKU patient should follow the PKU diet.
    • A. 

      Until they are 10 years old

    • B. 

      Until they are 25 years old

    • C. 

      For life.

  • 9. 
    Patients with amino acid disorders other than PKU present acutely ill.
    • A. 

      True

    • B. 

      False

  • 10. 
    Which number represents most accurately the average amount of protein coming from medical food in the case of a non-PKU diet.
    • A. 

      80%

    • B. 

      50%

    • C. 

      20%

  • 11. 
    Name the offending amino acid(s) in tyrosinemia.
    • A. 

      Phenylalanine and tyrosine

    • B. 

      Tyrosine

    • C. 

      Valine and tyrosine

  • 12. 
    In long-chain fatty acid oxidation disorders, which clinical symptoms would you NOT see during an acute episode associated with illness or prolonged fasting?
    • A. 

      Hypoglycemia

    • B. 

      Excessive ketone production

    • C. 

      Vomiting

    • D. 

      Lethargy

  • 13. 
    Supplementation with Carnitine is always necessary in which disorder:
    • A. 

      LCHADD

    • B. 

      VLCADD

    • C. 

      MCADD

    • D. 

      SCADD

    • E. 

      None of the above

  • 14. 
    For a 2 year old child with LCHADD, the following is NOT recommended during illness:
    • A. 

      Give him 2 to 3 oz of Pedialyte every 3 hours.

    • B. 

      If the child is vomiting and doesn’t seem to stop, it is better to wait until the next day to see the doctor because he might get over the illness by then.

    • C. 

      If the child is sleepy, let him sleep all night since he needs the rest

    • D. 

      B and c

    • E. 

      All of the above

  • 15. 
    Retinitis pigmentosa is a possible long-term complication for which disorder:
    • A. 

      MCADD

    • B. 

      SCADD

    • C. 

      VLCADD

    • D. 

      LCHADD

    • E. 

      Both c and d

  • 16. 
    Is Monogen indicated for MCADD diets?
    • A. 

      True

    • B. 

      False

  • 17. 
    Which of the following is NOT characteristic of an LCHADD patient’s diet?
    • A. 

      Reduce total fat

    • B. 

      Reduce LCT

    • C. 

      Reduce MCT

    • D. 

      All of the above

  • 18. 
    A recent study found that fewer abnormal acylcarnitines were produced in fibroblasts if ___________ was used as the EFA source.
    • A. 

      Flax oil

    • B. 

      Safflower oil with flax oil

    • C. 

      Flax oil and walnut oil

    • D. 

      Soy oil

    • E. 

      Canola oil

  • 19. 
    Which EFA source provides the best N6-N3 ratio? 
    • A. 

      Flax oil

    • B. 

      Walnut oil

    • C. 

      Soy oil

  • 20. 
    When monitoring EFAs, which reflects current (last few days) of intake? 
    • A. 

      Whole blood

    • B. 

      Plasma

    • C. 

      Either

  • 21. 
    Oleic acid production is reduced with EFA deficiency.
    • A. 

      True

    • B. 

      False

  • 22. 
    How much protein (PE) per 100 grams is in the new Periflex Infant with DHA & ARA?
    • A. 

      10 g PE

    • B. 

      8.33 g PE

    • C. 

      13 g PE

    • D. 

      25 g PE

  • 23. 
    Periflex Infant contains ____ gm DHA & ____ gm ARA per 100 gm product?
    • A. 

      2g, 35g

    • B. 

      0.2g, 0.35g

    • C. 

      0.2g, 3.5g

    • D. 

      None of the Above

  • 24. 
    Periflex Junior is designed to meet the nutritional needs of what age range?
    • A. 

      0-12 months

    • B. 

      1-10 years

    • C. 

      1-8 years

    • D. 

      9+ years

  • 25. 
    How much protein (PE) per 100 g is in the new Periflex Junior?
    • A. 

      20 g PE

    • B. 

      25 g PE

    • C. 

      35 g PE

    • D. 

      40 g PE

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