Cystic Fibrosis Quiz: Can You Manage The Care?

1. What is the inheritance pattern of Cystic Fibrosis?

Autosomal dominant

Autosomal recessive

X-linked dominant

X-linked recessive

2. Which organ system is primarily affected in Cystic Fibrosis?

Cardiovascular system

Respiratory and digestive systems

Nervous system

Renal system

3. Thick, viscous secretions in Cystic Fibrosis result from dysfunction of which type of glands?

Sebaceous glands

Sweat glands

Exocrine glands

Endocrine glands

4. Cystic Fibrosis is caused by a mutation in which gene?

CFTR gene

BRCA1 gene

FEV1 gene

HEXA gene

5. Life expectancy for individuals with Cystic Fibrosis has significantly improved due to advances in which area?

Gene therapy alone

Multidisciplinary care and medications

Lung transplantation only

Dietary management only

6. Pancreatic enzymes are replaced in Cystic Fibrosis patients to improve which process?

Nutrient absorption

Insulin secretion

Glucose metabolism

Bile production

7. Which pulmonary complication is the leading cause of death in Cystic Fibrosis?

Asthma

Chronic airway infection and bronchiectasis

Spontaneous pneumothorax

Pulmonary embolism

8. Pseudomonas aeruginosa colonization in Cystic Fibrosis airways is typically treated with which class of antibiotics?

Penicillins only

Aminoglycosides and fluoroquinolones

Cephalosporins only

Macrolides only

9. Ivacaftor is a CFTR modulator used in Cystic Fibrosis. What does it do?

Destroys bacteria in airways

Improves protein folding and channel function

Replaces pancreatic enzymes

Reduces inflammation

10. Distal intestinal obstruction syndrome (DIOS) in Cystic Fibrosis is treated with which intervention?

NPO status and surgery immediately

Polyethylene glycol and increased hydration

Antibiotics only

Pancreatic enzyme reduction

Submit

13. Cystic Fibrosis patients are at increased risk for which bone condition?

Osteoporosis

Osteomyelitis

Osteomalacia

Paget's disease

Submit

15. Which nutritional support is most important for Cystic Fibrosis patients?

Low-fat diet

High-calorie, high-protein diet

Liquid diet only

Low-sodium diet

Submit

19. Which pancreatic complication is most common in Cystic Fibrosis patients?

Acute pancreatitis

Pancreatic insufficiency

Pancreatic cancer

Pancreatic necrosis

Submit

Cystic Fibrosis Quiz: Can You Manage the Care?

1. What is the inheritance pattern of Cystic Fibrosis?

2.

What first name or nickname would you like us to use?

2. Which organ system is primarily affected in Cystic Fibrosis?

3. Thick, viscous secretions in Cystic Fibrosis result from dysfunction of which type of glands?

4. Cystic Fibrosis is caused by a mutation in which gene?

5. Life expectancy for individuals with Cystic Fibrosis has significantly improved due to advances in which area?

6. Pancreatic enzymes are replaced in Cystic Fibrosis patients to improve which process?

7. Which pulmonary complication is the leading cause of death in Cystic Fibrosis?

8. Pseudomonas aeruginosa colonization in Cystic Fibrosis airways is typically treated with which class of antibiotics?

9. Ivacaftor is a CFTR modulator used in Cystic Fibrosis. What does it do?

10. Distal intestinal obstruction syndrome (DIOS) in Cystic Fibrosis is treated with which intervention?

11. Psychosocial support and adherence to treatment regimens are critical nursing interventions for Cystic Fibrosis patients because the condition requires ____.

12. DNase (dornase alfa) is an inhaled medication for Cystic Fibrosis that breaks down extracellular ____.

13. Cystic Fibrosis patients are at increased risk for which bone condition?

14. Fat-soluble vitamins (A, D, E, K) must be supplemented in Cystic Fibrosis because of impaired ____.

15. Which nutritional support is most important for Cystic Fibrosis patients?

16. Meconium ileus in newborns is a classic presentation associated with Cystic Fibrosis. This condition involves ____.

17. Chest physiotherapy and airway clearance techniques are essential for Cystic Fibrosis patients. The primary goal is to ____.

18. Cystic Fibrosis-related diabetes (CFRD) develops due to pancreatic ____.

19. Which pancreatic complication is most common in Cystic Fibrosis patients?

20. The sweat chloride test is the gold standard diagnostic test for Cystic Fibrosis. A positive result shows chloride levels above ____.