Cystic Fibrosis Quiz: Can You Manage The Care?

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3. Life expectancy for individuals with Cystic Fibrosis has significantly improved due to advances in which area?

Gene therapy alone

Multidisciplinary care and medications

Lung transplantation only

Dietary management only

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5. Cystic Fibrosis patients are at increased risk for which bone condition?

Osteoporosis

Osteomyelitis

Osteomalacia

Paget's disease

6. Distal intestinal obstruction syndrome (DIOS) in Cystic Fibrosis is treated with which intervention?

NPO status and surgery immediately

Polyethylene glycol and increased hydration

Antibiotics only

Pancreatic enzyme reduction

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8. Which nutritional support is most important for Cystic Fibrosis patients?

Low-fat diet

High-calorie, high-protein diet

Liquid diet only

Low-sodium diet

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10. Ivacaftor is a CFTR modulator used in Cystic Fibrosis. What does it do?

Destroys bacteria in airways

Improves protein folding and channel function

Replaces pancreatic enzymes

Reduces inflammation

11. Cystic Fibrosis is caused by a mutation in which gene?

CFTR gene

BRCA1 gene

FEV1 gene

HEXA gene

12. Pseudomonas aeruginosa colonization in Cystic Fibrosis airways is typically treated with which class of antibiotics?

Penicillins only

Aminoglycosides and fluoroquinolones

Cephalosporins only

Macrolides only

13. Which pulmonary complication is the leading cause of death in Cystic Fibrosis?

Asthma

Chronic airway infection and bronchiectasis

Spontaneous pneumothorax

Pulmonary embolism

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15. Pancreatic enzymes are replaced in Cystic Fibrosis patients to improve which process?

Nutrient absorption

Insulin secretion

Glucose metabolism

Bile production

16. Which pancreatic complication is most common in Cystic Fibrosis patients?

Acute pancreatitis

Pancreatic insufficiency

Pancreatic cancer

Pancreatic necrosis

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18. Thick, viscous secretions in Cystic Fibrosis result from dysfunction of which type of glands?

Sebaceous glands

Sweat glands

Exocrine glands

Endocrine glands

19. Which organ system is primarily affected in Cystic Fibrosis?

Cardiovascular system

Respiratory and digestive systems

Nervous system

Renal system

20. What is the inheritance pattern of Cystic Fibrosis?

Autosomal dominant

Autosomal recessive

X-linked dominant

X-linked recessive

Cystic Fibrosis Quiz: Can You Manage the Care?

1. Chest physiotherapy and airway clearance techniques are essential for Cystic Fibrosis patients. The primary goal is to ____.

2.

What first name or nickname would you like us to use?

2. Psychosocial support and adherence to treatment regimens are critical nursing interventions for Cystic Fibrosis patients because the condition requires ____.

3. Life expectancy for individuals with Cystic Fibrosis has significantly improved due to advances in which area?

4. DNase (dornase alfa) is an inhaled medication for Cystic Fibrosis that breaks down extracellular ____.

5. Cystic Fibrosis patients are at increased risk for which bone condition?

6. Distal intestinal obstruction syndrome (DIOS) in Cystic Fibrosis is treated with which intervention?

7. Fat-soluble vitamins (A, D, E, K) must be supplemented in Cystic Fibrosis because of impaired ____.

8. Which nutritional support is most important for Cystic Fibrosis patients?

9. Meconium ileus in newborns is a classic presentation associated with Cystic Fibrosis. This condition involves ____.

10. Ivacaftor is a CFTR modulator used in Cystic Fibrosis. What does it do?

11. Cystic Fibrosis is caused by a mutation in which gene?

12. Pseudomonas aeruginosa colonization in Cystic Fibrosis airways is typically treated with which class of antibiotics?

13. Which pulmonary complication is the leading cause of death in Cystic Fibrosis?

14. Cystic Fibrosis-related diabetes (CFRD) develops due to pancreatic ____.

15. Pancreatic enzymes are replaced in Cystic Fibrosis patients to improve which process?

16. Which pancreatic complication is most common in Cystic Fibrosis patients?

17. The sweat chloride test is the gold standard diagnostic test for Cystic Fibrosis. A positive result shows chloride levels above ____.

18. Thick, viscous secretions in Cystic Fibrosis result from dysfunction of which type of glands?

19. Which organ system is primarily affected in Cystic Fibrosis?

20. What is the inheritance pattern of Cystic Fibrosis?