Medullary Cystic Disease - Abdomen B Quiz On 4/4/11

16 Questions

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Abdomen Quizzes & Trivia

Questions and Answers
  • 1. 
    Medullary has to do with the __________ which appear very echogenic in medullary cystic disease.
  • 2. 
    __________  ___________  ___________ is a common benign condition that leads to cystic dilation of the distal collecting tubules in the medulla. These ectatic tubules may be imaged with sono, but are best seen on urography (X-ray).
  • 3. 
    Medullary sponge kidney is a:
    • A. 

      Hereditary, autosomal recessive defect

    • B. 

      Congenital, autosomal dominant defect

    • C. 

      Hereditary, autosomal dominant defect

    • D. 

      Congenital, autosomal recessive defect

  • 4. 
    Medullary sponge kidney usually presents in ________ to ________  ________ adults.
  • 5. 
    Clinically, patients with medullary sponge kidney are usually asymptomatic. However, if there is a stone present, they may present with:
    • A. 

      Decreased hematocrit

    • B. 

      Pain

    • C. 

      Hydronephrosis

    • D. 

      Infection

    • E. 

      Hematuria

  • 6. 
    Because the very distal portion of the tubules is what is cystic, medullary sponge kidney is very easy to diagnose with sono.
    • A. 

      True

    • B. 

      False

  • 7. 
    In medullary sponge kidney, the medullary pyramids appear highly __________ (anechoic, complex, echogenic?) ________ (with or without?) shadowing and possible posterior acoustic enhancement.
  • 8. 
    A complication of medullary sponge kidney when stones and calcium deposit within the dilated tubules is called __________  ___________.
  • 9. 
    If stones are present in a patient with medullary sponge kidney, there will be shadowing and possibly hydro (proximal to where the stone is).
    • A. 

      True

    • B. 

      False

  • 10. 
    The two types of medullary cystic disease are:
  • 11. 
    Uremic Medullary Cystic Disease is a rare, progressive, ...
    • A. 

      Hereditary, autosomal recessive disease

    • B. 

      Hereditary, autosomal dominant or recessive disease

    • C. 

      Congenital, autosomal dominant disease

    • D. 

      Hereditary, autosomal dominant disease

    • E. 

      Congenital, autosomal recessive disease

  • 12. 
    Autosomal Dominant:  onset is seen in...
    • A. 

      Children

    • B. 

      Adults

  • 13. 
    Clinically, patients with uremic medullary cytic disease present with:
    • A. 

      Salt wasting (salt loss)

    • B. 

      Anemia

    • C. 

      Oliguria

    • D. 

      Progressive azotemia

    • E. 

      Polyuria

  • 14. 
    ________ and ________ are characterized by abnormal levels of urea, creatinine, various body waste compounds, and other nitrogen rich compounds in the blood as a result of insufficient filtering of the blood by the kidneys.  These words can be used synonymously.
  • 15. 
    Uremic Medullary Cystic Disease is AKA ______________.
  • 16. 
    Which medullary cystic disease do the following characteristics describe? Discrete cysts confined to medulla measuring up to 2 cm in size (can be micro or macro). Presence of variable number of cysts in the medulla. With microcysts the sinus will appear widened. Associated with significant cortical atrophy and interstitial edema. Eventually progresses to renal failure. If bilateral: Normal or smaller size kidneys with a thin cortex and loss of cortical medullary distinction. In advanced stages, the kidney appears small with increased parenchymal echogenicity and total loss of cortical medullary distinction.