Which of the following pulmonary abnormalities is the greatest risk for the client based on the findings below?
A 9-year-old boy was identified in childhood as having an elevated sweat chloride. Though he appeared to be a normal term baby, his neonatal course was complicated by the development of meconium ileus. Throughout childhood, he has experienced multiple increasingly severe bouts of pneumonia with a productive cough, often with Pseudomonas aeruginosa, and later Burkholderia cepacea, cultured from sputum.
A. Adenocarcinoma B. Bronchiectasis C. Lymphangiectasis D. Pleural fibrous plaques E. Pneumocystis carinii (jiroveci) pneumonia F. Pneumothorax
Bronchiectasis -(b) correct. the chronic lung disease of cystic fibrosis often includes bronchiectasis, a disease characterized by inflammation with obstruction and dilation and destruction of bronchi. this process is diffuse throughout the lungs. the loss of pulmonary vascular bed with progressive bronchiectasis can lead to pulmonary hypertension and cor pulmonale.(a) incorrect. the incidence of lung cancer is not increased with cystic fibrosis.(c) incorrect. dilation of lymphatics is an infrequent occurrence with mediastinal masses such as lymphomas.(d) incorrect. pleural plaques are most frequently seen with pneumoconioses.(e) incorrect. patients with cystic fibrosis usually have lung infections with bacteria such as pseudomonas.(f) incorrect. pneumonias with cystic fibrosis are unlikely to produce pneumothorax. no bullae form.